Utrophin correlates with disease severity in Duchenne muscular dystrophy.

Guiraud S., Davies K.

This month in Med, the description of an unusually severely affected DMD patient suffering from a large deletion in the dystrophin gene confirms that absence of utrophin worsens the dystrophy and supports the concept that utrophin upregulation ameliorates the pathology. This study may guide the development of dystrophin-based gene therapies.

DOI

10.1016/j.medj.2023.03.005

Type

Journal article

Journal

Med

Publication Date

14/04/2023

Volume

4

Pages

220 - 222

Keywords

Humans, Muscular Dystrophy, Duchenne, Dystrophin, Utrophin, Up-Regulation, Patient Acuity

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